Types of Congenital Heart Disease

Click on the hyperlinked disease titles and the diagram indications to be transferred to The Children's Heart Institute, The University of Utah's Medical Education Program, or the University of Kansas' website for excellent diagramatic depictions and photographs of these disorders.


Aortic Coarctation

*color diagram Narrowing of the aortic lumen leads to outflow obstruction, either proximal or distal to the ductus.
Double Inlet Ventricle   Both atria connect to only one ventricle chamber by either two separate atrioventricular valves or a common atrioventricular valve (Pediheart, 2001). Double Inlet Ventricle results in outflow obstruction to the pulmonary artery even to the severity of pulmonary atresia (complete obstruction).
Great Vessel Transposition *color diagram Left-to-right shunting occurs because the pulmonary artery arises from the left ventricle and the aorta arises from the right ventricle. This causes a high force of blood to be pumped into the lungs and a lower relative force to the body.
Epstein's Anomaly   Displacement of the tricuspid valve causing leakage and regurgitation. The right atrium is large and the right ventricle is unusually small. The infant will appear blue from cyanosis because there is not enough blood being pumped to the pulmonary arteries (Abdallah, 2001).
Hypoplastic Left Heart Syndrome   A severely underdeveloped left ventricle (which usually pumps blood to the body); proves fatal without a Norton Procedure or cardiac transplantation.
Patent Ductus Arteriosus   Left-to-right shunting occurs when the ductus arteriosus does not close after birth as it should. This causes increased pulmonary blood flow (Suddaby, 2001).
Septal Defects
*color diagram A hole in the membrane (septum) separating the two atria or the two ventricles, which usually results in left-to-right shunting. Septal defects also increase the risk for infective endocarditis.

Tetralogy of Fallot

*black and white diagram
*color diagram
Four characteristics: 1) Ventral septal defect, 2) overriding ascending aorta, 3) pulmonic stenosis, and 4) right ventricular hypertrophy.
TAPVR (Total Anomalous Pulmonary Venous Return)   The four pulmonary veins that bring oxygenated blood back to the heart do not connect with the left atrium as they should, instead connecting with a coronary sinus or other site, creating a mixing of oxygen-rich and oxygen-poor blood (vciweb, 2001).
Tricuspid Atresia   Complete maldevelopment of the right atrioventricular valve; an intraventricular foramen is present between the maldeveloped right ventricle and the left ventricle (Pediheart 2001).

Truncus Arteriosus


*color diagram
A ventral septal defect, in combination with incomplete separation of aortic and pulmonary artery blood, creates a mixed oxygenated/deoxygenated blood supply and right-to-left shunting. Infants in this condition will undergo congestive heart failure, and will be sweating and breathing rapidly (Abdallah, 2001).
Valve Stenosis and Prolapse   Narrowing of the valves which can also cause reguritation of blood back into the chamber from which it just came.

 

 

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